El Angiofibroma nasofaríngeo juvenil es un tumor benigno vascular (pero que tardíamente Se localiza en la pared posterolateral de la grita nasal a nivel del vínculo de la apófisis esfenoidal del hueso palatino. Esta localización conforma el. Nasal cavity, paranasal sinuses, nasopharynx – Nasopharyngeal angiofibroma. Juvenile nasopharyngeal angiofibroma (JNA) is a rare and benign but locally in the nasopharynx and nasal cavity, leading to manifestations such as nasal.

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Operative treatment of nasopharyngeal angiofibroma with intracranial extension is one of the major challenges of ENT and neurosurgical practice.

Juvenile nasopharyngeal angiofibroma | Radiology Reference Article |

The 3 patients who underwent combined surgeries experienced intraoperative bleeding, requiring nasal packing and replacement juvdnil blood products during surgery. They may be locally aggressive. Invasion of the intracranial region may lead to cranial nerve palsy.

This website is intended for pathologists and laboratory personnel, who jjuvenil that medical juvenll is imperfect and must be interpreted using reasonable medical judgment. Mean patient age was JNA is classified as Type I when the tumor is restricted to the nasal cavity and the nasopharynx without bone destruction, Type II when the tumor invades the pterygomaxillary fossa and maxillary, sphenoidal and ethmoid sinuses with bone destruction, Type III when the tumor invades the infratemporal fossa, the orbit, and the parasellar region but remains lateral to the cavernous sinus nsal Type IV when the tumor invades the cavernous sinus, the optic chiasma and the pituitary fossa.

Epistaxis, rhinorrhea and pain may also be seen. Service chief medical residency in Otorhinolaryngology, Universidade Federal de Sergipe. The location and size of the tumor and feeding vessels are clearly demonstrated by this technique.


Nasopharyngeal angiofibroma: our experience and literature review

Angiography, although not essential, is often useful in both defining the feeding vessels as well as in preoperative embolisation. Well circumscribed but unencapsulated polypoid fibrous mass, bleeds severely on manipulation and biopsy, may occlude nares Spongy cut surface. MRI is superior to CT for detecting soft tissue extension of the tumor intracranially.

Full occupation of the pterygomaxillary fossa, anterior displacement of the posterior wall of the maxillary antrum. The prevalence in males may be explained by high androgen receptor AR expression naxal that JNA is androgen dependent. Genetic alterations in juvenile nasopharyngeal angiofibromas. Many studies highlight the benefit of preoperative arterial embolization to control bleeding intraoperative 16,29, Mast cells and T-lymphocytes in juvenile angiofibromas. Analysis of these 13 patients suggests that fully endoscopic surgery is viable even in advanced cases of JNA.

Angiofibroma nasofaríngeo juvenil

In this study, we have described our experience in treating 20 patients with nasopharyngeal angiofibromas in the Department of Otorhinolaryngology. Fisch classification, however, is currently accepted. Use of neuronavigation techniques, intraoperative MRI, customized instruments, and ever-increasing surgical experience are all factors contributing to further advancements in this field, toward safer and more effective endoscopic approaches.

Removal is important in preventing nasal obstruction and recurrent epistaxis.

Treatment trends in patients during 40 years. He also complained of difficulty in breathing since 6—7 months.

It impinges on adjacent structures and causes pressure erosion of bone. The surgical management of extensive nasopharyngeal angiofibromas with the infratemporal fossa approach.

Juvenile nasopharyngeal angiofibroma

Disease definition Juvenile nasopharyngeal angiofibroma JNA is a rare and benign but kuvenil aggressive fibrovascular tumor arising from the posterolateral wall of the nasopharynx, which affects mainly young and adolescent males onset usually occurring between years of angikfibroma and that presents as a mass in the nasopharynx and nasal cavity, leading to manifestations such as nasal obstruction, epistaxis, profound facial swelling, proptosis or diplopia.


Home About Us Advertise Amazon. Endoscopic approach for excision of juvenile nasopharyngeal angiofibroma: Therefore, the irreversible lesions found in this group may ahgiofibroma been the result of the technical challenges encountered during surgery.

Extensive bony destruction is usually not a feature, but rather bone is remodelled or resorbed. Continuous growth involves the sphenoidal sinus, nasal fossa and middle turbinate, pterygomaxillary fossa and the posterior wall of the maxillary sinus as seen in the present case.

Endoscopic surgery alone or with other conventional techniques was safe for the treatment of angiofibromas angiotibroma different stages. April 08, ; Accepted: This relatively low blood loss may be due to the use of surgical endoscopy, providing better control of bleeding than open surgery, with or without endoscopy. This makes it possible to precisely stage JNA. Indian J Dent Res. Erosion of the skull base with minimal intracranial extension.

A wait and watch policy with periodic imaging may thus postpone or eliminate the need for surgery and reduce morbidity. Juvenile nasopharyngeal angiofibroma originates in the sphenopalatine forame, causing epistaxes and angiofobroma obstruction.

Biological distinctions between juvenile nasopharyngeal angiofibroma and vascular malformation: Irradiation may be an option if surgery is not possible or only incomplete resection achieved 2,4,6.